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Drosophila Carrying Pex3 or Pex16 Mutations Are Models of Zellweger Syndrome That Reflect Its Symptoms Associated with the Absence of Peroxisomes
The peroxisome biogenesis disorders (PBDs) are currently difficult-to-treat multiple-organ dysfunction disorders that result from the defective biogenesis of peroxisomes. Genes encoding Peroxins, which are required for peroxisome biogenesis or functions, are known causative genes of PBDs. The human...
Autores principales: | Nakayama, Minoru, Sato, Hiroyasu, Okuda, Takayuki, Fujisawa, Nao, Kono, Nozomu, Arai, Hiroyuki, Suzuki, Emiko, Umeda, Masato, Ishikawa, Hiroyuki O., Matsuno, Kenji |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3149631/ https://www.ncbi.nlm.nih.gov/pubmed/21826223 http://dx.doi.org/10.1371/journal.pone.0022984 |
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