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Parry-Romberg Syndrome with En Coup de Sabre
Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de s...
Autores principales: | , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Korean Dermatological Association; The Korean Society for Investigative Dermatology
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3162264/ https://www.ncbi.nlm.nih.gov/pubmed/21909205 http://dx.doi.org/10.5021/ad.2011.23.3.342 |
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author | Jun, Jae Hun Kim, Ho Youn Jung, Han Jin Lee, Weon Ju Lee, Seok-Jong Kim, Do Won Kim, Moon Bum Kim, Byung Soo |
author_facet | Jun, Jae Hun Kim, Ho Youn Jung, Han Jin Lee, Weon Ju Lee, Seok-Jong Kim, Do Won Kim, Moon Bum Kim, Byung Soo |
author_sort | Jun, Jae Hun |
collection | PubMed |
description | Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de sabre. This is a report of the author's experiences with PRS accompanying en coup de sabre, and a review of the ongoing considerable debate associated with these two entities. Case 1 was a 37-year-old woman who had right hemifacial atrophy with unilateral en coup de sabre for seven years. Fat grafting to her atrophic lip had been conducted, and steroid injection had been performed on the indurated plaque of the forehead. Case 2 was a 29-year-old woman who had suffered from right hemifacial atrophy and bilateral en coup de sabre for 18 years. Surgical corrections such as scapular osteocutaneous flap and mandible/maxilla distraction showed unsatisfying results. |
format | Online Article Text |
id | pubmed-3162264 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2011 |
publisher | Korean Dermatological Association; The Korean Society for Investigative Dermatology |
record_format | MEDLINE/PubMed |
spelling | pubmed-31622642011-09-09 Parry-Romberg Syndrome with En Coup de Sabre Jun, Jae Hun Kim, Ho Youn Jung, Han Jin Lee, Weon Ju Lee, Seok-Jong Kim, Do Won Kim, Moon Bum Kim, Byung Soo Ann Dermatol Case Report Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de sabre. This is a report of the author's experiences with PRS accompanying en coup de sabre, and a review of the ongoing considerable debate associated with these two entities. Case 1 was a 37-year-old woman who had right hemifacial atrophy with unilateral en coup de sabre for seven years. Fat grafting to her atrophic lip had been conducted, and steroid injection had been performed on the indurated plaque of the forehead. Case 2 was a 29-year-old woman who had suffered from right hemifacial atrophy and bilateral en coup de sabre for 18 years. Surgical corrections such as scapular osteocutaneous flap and mandible/maxilla distraction showed unsatisfying results. Korean Dermatological Association; The Korean Society for Investigative Dermatology 2011-08 2011-08-06 /pmc/articles/PMC3162264/ /pubmed/21909205 http://dx.doi.org/10.5021/ad.2011.23.3.342 Text en Copyright © 2011 Korean Dermatological Association; The Korean Society for Investigative Dermatology http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Jun, Jae Hun Kim, Ho Youn Jung, Han Jin Lee, Weon Ju Lee, Seok-Jong Kim, Do Won Kim, Moon Bum Kim, Byung Soo Parry-Romberg Syndrome with En Coup de Sabre |
title | Parry-Romberg Syndrome with En Coup de Sabre |
title_full | Parry-Romberg Syndrome with En Coup de Sabre |
title_fullStr | Parry-Romberg Syndrome with En Coup de Sabre |
title_full_unstemmed | Parry-Romberg Syndrome with En Coup de Sabre |
title_short | Parry-Romberg Syndrome with En Coup de Sabre |
title_sort | parry-romberg syndrome with en coup de sabre |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3162264/ https://www.ncbi.nlm.nih.gov/pubmed/21909205 http://dx.doi.org/10.5021/ad.2011.23.3.342 |
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