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Pulmonary medium vessel vasculitis in an 11 year old boy: Hughes Stovin syndrome as a variant of polyarteritis nodosa?
We present the case of an 11-year-old boy presenting with haemoptysis, dyspnoea and weight loss as a manifestation of isolated pulmonary vasculitis, leading to pulmonary hypertension. He also appeared to have a longstanding dural venous sinus thrombosis. This rare presentation, especially in childho...
Autores principales: | de Vries, Willemien, Koppelman, Gerard H, Roofthooft, Marc TR, Bootsma, Hendrika, Leijsma, Martha K, Armbrust, Wineke |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3170265/ https://www.ncbi.nlm.nih.gov/pubmed/21816089 http://dx.doi.org/10.1186/1546-0096-9-19 |
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