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Prolonged survival after splenectomy in Wiskott-Aldrich syndrome: a case report

Wiskott-Aldrich syndrome is a rare X-linked immunodeficiency disorder that is characterized by a variable clinical phenotype. Matched donor bone marrow transplantation is currently the only curative therapeutic option. We present the case of a 24-year-old male who was diagnosed at the age of seven w...

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Detalles Bibliográficos
Autores principales:	Syrigos, Kostas N, Makrilia, Nektaria, Neidhart, Jeffrey, Moutsos, Michael, Tsimpoukis, Sotirios, Kiagia, Maria, Saif, Muhammad W
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2011
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3179709/ https://www.ncbi.nlm.nih.gov/pubmed/21906397 http://dx.doi.org/10.1186/1824-7288-37-42

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