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A Drosophila model for the Zellweger spectrum of peroxisome biogenesis disorders

Human peroxisome biogenesis disorders are lethal genetic diseases in which abnormal peroxisome assembly compromises overall peroxisome and cellular function. Peroxisomes are ubiquitous membrane-bound organelles involved in several important biochemical processes, notably lipid metabolism and the use...

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Detalles Bibliográficos
Autores principales:	Mast, Fred D., Li, Jing, Virk, Maninder K., Hughes, Sarah C., Simmonds, Andrew J., Rachubinski, Richard A.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Company of Biologists Limited 2011
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3180231/ https://www.ncbi.nlm.nih.gov/pubmed/21669930 http://dx.doi.org/10.1242/dmm.007419

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