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Regulating complement in the kidney: insights from CFHR5 nephropathy

Complement factor H related protein 5 (CFHR5) nephropathy is a monogenic disorder of complement regulation that is endemic in Cyprus. The disease is characterised by haematuria, C3 glomerulonephritis and kidney failure. Its identification suggests a role for the CFHR5 protein in the regulation of co...

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Detalles Bibliográficos
Autores principales:	Gale, Daniel P., Pickering, Matthew C.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Company of Biologists Limited 2011
Materias:	Clinical Puzzle
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3209641/ https://www.ncbi.nlm.nih.gov/pubmed/22065842 http://dx.doi.org/10.1242/dmm.008052

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