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Dysfunction of axonal membrane conductances in adolescents and young adults with spinal muscular atrophy
Spinal muscular atrophy is distinct among neurodegenerative conditions of the motor neuron, with onset in developing and maturing patients. Furthermore, the rate of degeneration appears to slow over time, at least in the milder forms. To investigate disease pathophysiology and potential adaptations,...
Autores principales: | Farrar, Michelle A., Vucic, Steve, Lin, Cindy S.-Y., Park, Susanna B., Johnston, Heather M., du Sart, Desirée, Bostock, Hugh, Kiernan, Matthew C. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3212713/ https://www.ncbi.nlm.nih.gov/pubmed/21926101 http://dx.doi.org/10.1093/brain/awr229 |
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