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The genetics of pulmonary arterial hypertension in the post-BMPR2 era
Pulmonary arterial hypertension (PAH) is a rapidly progressive and fatal disease for which there is an ever-expanding body of genetic and related pathophysiological information on disease pathogenesis. The most common single culprit gene known is BMPR2, and animal models of the disease in several fo...
Autores principales: | Fessel, Joshua P., Loyd, James E., Austin, Eric D. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3224422/ https://www.ncbi.nlm.nih.gov/pubmed/22140620 http://dx.doi.org/10.4103/2045-8932.87293 |
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