Asymptomatic cardiac rhabdomyoma in neonates: is surgery indicated?

BACKGROUND: Neonatal Tuberose sclerosis complex may be associated with symptomatic cardiac rhabdomyomas. Cardiac rhabdomyomas are the most common cardiac tumours. The symptoms include haemodynamic instability and life threatening arrhythmias usually requiring early surgical intervention. RESULTS: We...

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Detalles Bibliográficos
Autores principales: Etuwewe, B, John, CM, Abdelaziz, M
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2009
Materias:
Original Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3232602/
https://www.ncbi.nlm.nih.gov/pubmed/22368553
Descripción
Sumario:BACKGROUND: Neonatal Tuberose sclerosis complex may be associated with symptomatic cardiac rhabdomyomas. Cardiac rhabdomyomas are the most common cardiac tumours. The symptoms include haemodynamic instability and life threatening arrhythmias usually requiring early surgical intervention. RESULTS: We report a case of a 32 week gestation newborn diagnosed with a right ventricular outflow tract mass and subsequently diagnosed with tuberose sclerosis that needed early surgical intervention. CONCLUSION: While this case needed early intervention, the need for surgical intervention in otherwise asymptomatic cases is debatable as neonatal cardiac rhabdomyomas can spontaneously regress.

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