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Immortalized pathological human myoblasts: towards a universal tool for the study of neuromuscular disorders
BACKGROUND: Investigations into both the pathophysiology and therapeutic targets in muscle dystrophies have been hampered by the limited proliferative capacity of human myoblasts. Isolation of reliable and stable immortalized cell lines from patient biopsies is a powerful tool for investigating path...
Autores principales: | Mamchaoui, Kamel, Trollet, Capucine, Bigot, Anne, Negroni, Elisa, Chaouch, Soraya, Wolff, Annie, Kandalla, Prashanth K, Marie, Solenne, Di Santo, James, St Guily, Jean Lacau, Muntoni, Francesco, Kim, Jihee, Philippi, Susanne, Spuler, Simone, Levy, Nicolas, Blumen, Sergiu C, Voit, Thomas, Wright, Woodring E, Aamiri, Ahmed, Butler-Browne, Gillian, Mouly, Vincent |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3235972/ https://www.ncbi.nlm.nih.gov/pubmed/22040608 http://dx.doi.org/10.1186/2044-5040-1-34 |
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