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Physiology and Pathophysiology of CLC-1: Mechanisms of a Chloride Channel Disease, Myotonia
The CLC-1 chloride channel, a member of the CLC-channel/transporter family, plays important roles for the physiological functions of skeletal muscles. The opening of this chloride channel is voltage dependent and is also regulated by protons and chloride ions. Mutations of the gene encoding CLC-1 re...
Autores principales: | Tang, Chih-Yung, Chen, Tsung-Yu |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi Publishing Corporation
2011
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3237021/ https://www.ncbi.nlm.nih.gov/pubmed/22187529 http://dx.doi.org/10.1155/2011/685328 |
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