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Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report

Epithelioid hemangioendothelioma (EHE) is a rare, well-differentiated endothelial tumor with intermediate malignancy which develops more frequently from the peripheral veins, generally in the lower limb. Bone EHE comprises less than 1% of the bone neoplasms. We present the case of a young man, 24-ye...

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Autores principales: Gherman, Claudia D, Fodor, Daniela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2011
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3251536/
https://www.ncbi.nlm.nih.gov/pubmed/22145982
http://dx.doi.org/10.1186/1746-1596-6-120
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author Gherman, Claudia D
Fodor, Daniela
author_facet Gherman, Claudia D
Fodor, Daniela
author_sort Gherman, Claudia D
collection PubMed
description Epithelioid hemangioendothelioma (EHE) is a rare, well-differentiated endothelial tumor with intermediate malignancy which develops more frequently from the peripheral veins, generally in the lower limb. Bone EHE comprises less than 1% of the bone neoplasms. We present the case of a young man, 24-year-old, with EHE of the forearm with secondary involvement of the distal radius. The location and the extension of the tumor allowed a wide excision, without the reconstruction of radius, followed by adjuvant radiotherapy, with a subsequent favorable evolution. Based on the clinical, radiographic, and pathological features of the EHE review, we concluded that it is difficult to adopt a standardized therapeutic approach due to the extremely low incidence of the bone involvement in EHE and the variable tendencies towards malignancy of this tumor. To our knowledge this is the third case of EHE with the involvement of the radius.
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spelling pubmed-32515362012-01-05 Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report Gherman, Claudia D Fodor, Daniela Diagn Pathol Case Report Epithelioid hemangioendothelioma (EHE) is a rare, well-differentiated endothelial tumor with intermediate malignancy which develops more frequently from the peripheral veins, generally in the lower limb. Bone EHE comprises less than 1% of the bone neoplasms. We present the case of a young man, 24-year-old, with EHE of the forearm with secondary involvement of the distal radius. The location and the extension of the tumor allowed a wide excision, without the reconstruction of radius, followed by adjuvant radiotherapy, with a subsequent favorable evolution. Based on the clinical, radiographic, and pathological features of the EHE review, we concluded that it is difficult to adopt a standardized therapeutic approach due to the extremely low incidence of the bone involvement in EHE and the variable tendencies towards malignancy of this tumor. To our knowledge this is the third case of EHE with the involvement of the radius. BioMed Central 2011-12-06 /pmc/articles/PMC3251536/ /pubmed/22145982 http://dx.doi.org/10.1186/1746-1596-6-120 Text en Copyright ©2011 Gherman and Fodor; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Gherman, Claudia D
Fodor, Daniela
Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
title Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
title_full Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
title_fullStr Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
title_full_unstemmed Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
title_short Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
title_sort epithelioid hemangioendothelioma of the forearm with radius involvement. case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3251536/
https://www.ncbi.nlm.nih.gov/pubmed/22145982
http://dx.doi.org/10.1186/1746-1596-6-120
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