Hereditary Sclerosing Poikiloderma

Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also,...

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Autores principales: Lee, Hyo Jin, Shin, Dong Hoon, Choi, Jong Soo, Kim, Ki Hong
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Academy of Medical Sciences 2012
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3271301/
https://www.ncbi.nlm.nih.gov/pubmed/22323875
http://dx.doi.org/10.3346/jkms.2012.27.2.225
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author Lee, Hyo Jin
Shin, Dong Hoon
Choi, Jong Soo
Kim, Ki Hong
author_facet Lee, Hyo Jin
Shin, Dong Hoon
Choi, Jong Soo
Kim, Ki Hong
author_sort Lee, Hyo Jin
collection PubMed
description Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
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spelling pubmed-32713012012-02-09 Hereditary Sclerosing Poikiloderma Lee, Hyo Jin Shin, Dong Hoon Choi, Jong Soo Kim, Ki Hong J Korean Med Sci Case Report Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP. The Korean Academy of Medical Sciences 2012-02 2012-01-27 /pmc/articles/PMC3271301/ /pubmed/22323875 http://dx.doi.org/10.3346/jkms.2012.27.2.225 Text en © 2012 The Korean Academy of Medical Sciences. http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Lee, Hyo Jin
Shin, Dong Hoon
Choi, Jong Soo
Kim, Ki Hong
Hereditary Sclerosing Poikiloderma
title Hereditary Sclerosing Poikiloderma
title_full Hereditary Sclerosing Poikiloderma
title_fullStr Hereditary Sclerosing Poikiloderma
title_full_unstemmed Hereditary Sclerosing Poikiloderma
title_short Hereditary Sclerosing Poikiloderma
title_sort hereditary sclerosing poikiloderma
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3271301/
https://www.ncbi.nlm.nih.gov/pubmed/22323875
http://dx.doi.org/10.3346/jkms.2012.27.2.225
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AT choijongsoo hereditarysclerosingpoikiloderma
AT kimkihong hereditarysclerosingpoikiloderma

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