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Idiopathic Adult Ileoileal and Ileocolic Intussusception in situs Inversus Totalis: A Rare Coincidence

Situs inversus totalis is a rare autosomal recessive congenital anomaly that is characterized by mirror image anatomy of the abdominal and thoracic organs. We report a case of a 28-year-old male with situs inversus totalis, who developed an idiopathic ileoileal and ileocolic intussusception, which w...

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Detalles Bibliográficos
Autores principales: Butt, Nazish, Shah, Syed H., Alvi, Abdul R., Tanveer-ul-Haq, Hassan, Saba
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3271699/
https://www.ncbi.nlm.nih.gov/pubmed/22249097
http://dx.doi.org/10.4103/1319-3767.91732
Descripción
Sumario:Situs inversus totalis is a rare autosomal recessive congenital anomaly that is characterized by mirror image anatomy of the abdominal and thoracic organs. We report a case of a 28-year-old male with situs inversus totalis, who developed an idiopathic ileoileal and ileocolic intussusception, which was diagnosed on computed tomography scan. Patient underwent successfully ileal resection and side-to-side functional anastomosis of ileum 12 cms from ileocecal junction. Postoperative course was uneventful. To the best of our knowledge, this is the first case of idiopathic adult intussusception with situs inversus totalis in the literature.