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Human Prion Diseases in The Netherlands (1998–2009): Clinical, Genetic and Molecular Aspects
Prion diseases are rare and fatal neurodegenerative disorders that can be sporadic, inherited or acquired by infection. Based on a national surveillance program in the Netherlands we describe here the clinical, neuropathological, genetic and molecular characteristics of 162 patients with neuropathol...
Autores principales: | Jansen, Casper, Parchi, Piero, Capellari, Sabina, Ibrahim-Verbaas, Carla A., Schuur, Maaike, Strammiello, Rosaria, Corrado, Patrizia, Bishop, Matthew T., van Gool, Willem A., Verbeek, Marcel M., Baas, Frank, van Saane, Wesley, Spliet, Wim G. M., Jansen, Gerard H., van Duijn, Cornelia M., Rozemuller, Annemieke J. M. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3340342/ https://www.ncbi.nlm.nih.gov/pubmed/22558438 http://dx.doi.org/10.1371/journal.pone.0036333 |
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