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Cholangiocyte cilia are abnormal in syndromic and non-syndromic biliary atresia

Biliary atresia is a neonatal disorder characterized by aggressive fibroinflammatory obliteration of the biliary tract. Approximately 20 percent of biliary atresia patients demonstrate left-right laterality defects (syndromic biliary atresia). Cilia participate in important physiologic functions in...

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Detalles Bibliográficos
Autores principales:	Chu, Andrew S., Russo, Pierre A., Wells, Rebecca G.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	2012
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3341539/ https://www.ncbi.nlm.nih.gov/pubmed/22301700 http://dx.doi.org/10.1038/modpathol.2011.212

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