Cargando…

True hermaphrodite presenting as primary amenorrhea

True hermaphrodite is one of the rare variety of disorders of sex development. Most of them are genotypically females (46 XX) and present as under virilized males. Features of hyperandrogenism are present in those reared as females. The commonest histological variety of gonad found in them is ovotes...

Descripción completa

Detalles Bibliográficos
Autores principales: Palo, Lal Bahadur, Daniel, Mary, Padma, Alaganandam, Sahoo, Jaya Prakash
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3401773/
https://www.ncbi.nlm.nih.gov/pubmed/22837933
http://dx.doi.org/10.4103/2230-8210.98031
_version_ 1782238652390178816
author Palo, Lal Bahadur
Daniel, Mary
Padma, Alaganandam
Sahoo, Jaya Prakash
author_facet Palo, Lal Bahadur
Daniel, Mary
Padma, Alaganandam
Sahoo, Jaya Prakash
author_sort Palo, Lal Bahadur
collection PubMed
description True hermaphrodite is one of the rare variety of disorders of sex development. Most of them are genotypically females (46 XX) and present as under virilized males. Features of hyperandrogenism are present in those reared as females. The commonest histological variety of gonad found in them is ovotestis, which is at risk for malignancy. We report a girl with 46 XY true hermaphrodite without ovotestis presenting as primary amenorrhea and isolated clitoromegaly in the absence of any other features of virilization.
format Online
Article
Text
id pubmed-3401773
institution National Center for Biotechnology Information
language English
publishDate 2012
publisher Medknow Publications & Media Pvt Ltd
record_format MEDLINE/PubMed
spelling pubmed-34017732012-07-26 True hermaphrodite presenting as primary amenorrhea Palo, Lal Bahadur Daniel, Mary Padma, Alaganandam Sahoo, Jaya Prakash Indian J Endocrinol Metab Case Report True hermaphrodite is one of the rare variety of disorders of sex development. Most of them are genotypically females (46 XX) and present as under virilized males. Features of hyperandrogenism are present in those reared as females. The commonest histological variety of gonad found in them is ovotestis, which is at risk for malignancy. We report a girl with 46 XY true hermaphrodite without ovotestis presenting as primary amenorrhea and isolated clitoromegaly in the absence of any other features of virilization. Medknow Publications & Media Pvt Ltd 2012 /pmc/articles/PMC3401773/ /pubmed/22837933 http://dx.doi.org/10.4103/2230-8210.98031 Text en Copyright: © Indian Journal of Endocrinology and Metabolism http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Palo, Lal Bahadur
Daniel, Mary
Padma, Alaganandam
Sahoo, Jaya Prakash
True hermaphrodite presenting as primary amenorrhea
title True hermaphrodite presenting as primary amenorrhea
title_full True hermaphrodite presenting as primary amenorrhea
title_fullStr True hermaphrodite presenting as primary amenorrhea
title_full_unstemmed True hermaphrodite presenting as primary amenorrhea
title_short True hermaphrodite presenting as primary amenorrhea
title_sort true hermaphrodite presenting as primary amenorrhea
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3401773/
https://www.ncbi.nlm.nih.gov/pubmed/22837933
http://dx.doi.org/10.4103/2230-8210.98031
work_keys_str_mv AT palolalbahadur truehermaphroditepresentingasprimaryamenorrhea
AT danielmary truehermaphroditepresentingasprimaryamenorrhea
AT padmaalaganandam truehermaphroditepresentingasprimaryamenorrhea
AT sahoojayaprakash truehermaphroditepresentingasprimaryamenorrhea