Churg-Strauss syndrome associated with AA amyloidosis: a case report

Churg Strauss syndrome is a rare systemic and pulmonary vasculitis exceptionally associated with AA amyloidosis. We report the case of a 65-year old woman with past medical history of asthma. She developed polyarthralgia, headache and purpura. A laboratory workout found hypereosinophilia (1150/µL),...

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Autores principales: Maamar, Mouna, Tazi-Mezalek, Zoubida, Harmouche, Hicham, El Hamany, Zitouna, Adnaoui, Mohammed, Aouni, Mohammed
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The African Field Epidemiology Network 2012
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3415051/
https://www.ncbi.nlm.nih.gov/pubmed/22891088
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author Maamar, Mouna
Tazi-Mezalek, Zoubida
Harmouche, Hicham
El Hamany, Zitouna
Adnaoui, Mohammed
Aouni, Mohammed
author_facet Maamar, Mouna
Tazi-Mezalek, Zoubida
Harmouche, Hicham
El Hamany, Zitouna
Adnaoui, Mohammed
Aouni, Mohammed
author_sort Maamar, Mouna
collection PubMed
description Churg Strauss syndrome is a rare systemic and pulmonary vasculitis exceptionally associated with AA amyloidosis. We report the case of a 65-year old woman with past medical history of asthma. She developed polyarthralgia, headache and purpura. A laboratory workout found hypereosinophilia (1150/µL), positive p-ANCA, microscopic haematuria and proteinuria at 2g/day. A diagnosis of Churg-Strauss syndrome was established based on five criteria of the American College of Rheumatology (ACR). Renal biopsy showed an important type AA amyloid deposit. The patient was treated with steroids with a good response of the vasculitis and amyloidosis with disappearance of the proteinuria.
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spelling pubmed-34150512012-08-13 Churg-Strauss syndrome associated with AA amyloidosis: a case report Maamar, Mouna Tazi-Mezalek, Zoubida Harmouche, Hicham El Hamany, Zitouna Adnaoui, Mohammed Aouni, Mohammed Pan Afr Med J Case Report Churg Strauss syndrome is a rare systemic and pulmonary vasculitis exceptionally associated with AA amyloidosis. We report the case of a 65-year old woman with past medical history of asthma. She developed polyarthralgia, headache and purpura. A laboratory workout found hypereosinophilia (1150/µL), positive p-ANCA, microscopic haematuria and proteinuria at 2g/day. A diagnosis of Churg-Strauss syndrome was established based on five criteria of the American College of Rheumatology (ACR). Renal biopsy showed an important type AA amyloid deposit. The patient was treated with steroids with a good response of the vasculitis and amyloidosis with disappearance of the proteinuria. The African Field Epidemiology Network 2012-06-11 /pmc/articles/PMC3415051/ /pubmed/22891088 Text en © Mouna Maamar et al. http://creativecommons.org/licenses/by/2.0 The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Maamar, Mouna
Tazi-Mezalek, Zoubida
Harmouche, Hicham
El Hamany, Zitouna
Adnaoui, Mohammed
Aouni, Mohammed
Churg-Strauss syndrome associated with AA amyloidosis: a case report
title Churg-Strauss syndrome associated with AA amyloidosis: a case report
title_full Churg-Strauss syndrome associated with AA amyloidosis: a case report
title_fullStr Churg-Strauss syndrome associated with AA amyloidosis: a case report
title_full_unstemmed Churg-Strauss syndrome associated with AA amyloidosis: a case report
title_short Churg-Strauss syndrome associated with AA amyloidosis: a case report
title_sort churg-strauss syndrome associated with aa amyloidosis: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3415051/
https://www.ncbi.nlm.nih.gov/pubmed/22891088
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