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Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases

Aceruloplasminemia is a rare autosomal recessive disease in which a mutation leads to the absence or dysfunction of ceruloplasmin. Deficiency of this enzyme leads to the accumulation of iron in various organs; aceruloplasminemia is usually characterized by diabetes, retinal degeneration and neurolog...

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Autores principales: Roberti, Maria do Rosário Ferraz, Borges Filho, Handel Meireles, Gonçalves, Cláudio Humberto, Lima, Flávio Leão
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Associação Brasileira de Hematologia e Hemoterapia 2011
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3415789/
https://www.ncbi.nlm.nih.gov/pubmed/23049345
http://dx.doi.org/10.5581/1516-8484.20110104
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author Roberti, Maria do Rosário Ferraz
Borges Filho, Handel Meireles
Gonçalves, Cláudio Humberto
Lima, Flávio Leão
author_facet Roberti, Maria do Rosário Ferraz
Borges Filho, Handel Meireles
Gonçalves, Cláudio Humberto
Lima, Flávio Leão
author_sort Roberti, Maria do Rosário Ferraz
collection PubMed
description Aceruloplasminemia is a rare autosomal recessive disease in which a mutation leads to the absence or dysfunction of ceruloplasmin. Deficiency of this enzyme leads to the accumulation of iron in various organs; aceruloplasminemia is usually characterized by diabetes, retinal degeneration and neurological disorders. Diagnosis is suspected by the presence of elevated levels of ferritin, anemia, decreased serum copper and absence of ceruloplasmin in serum. Treatment of aceruloplasminemia is mainly based on the control of iron overload.
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spelling pubmed-34157892012-10-04 Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases Roberti, Maria do Rosário Ferraz Borges Filho, Handel Meireles Gonçalves, Cláudio Humberto Lima, Flávio Leão Rev Bras Hematol Hemoter Case Report Aceruloplasminemia is a rare autosomal recessive disease in which a mutation leads to the absence or dysfunction of ceruloplasmin. Deficiency of this enzyme leads to the accumulation of iron in various organs; aceruloplasminemia is usually characterized by diabetes, retinal degeneration and neurological disorders. Diagnosis is suspected by the presence of elevated levels of ferritin, anemia, decreased serum copper and absence of ceruloplasmin in serum. Treatment of aceruloplasminemia is mainly based on the control of iron overload. Associação Brasileira de Hematologia e Hemoterapia 2011 /pmc/articles/PMC3415789/ /pubmed/23049345 http://dx.doi.org/10.5581/1516-8484.20110104 Text en http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Roberti, Maria do Rosário Ferraz
Borges Filho, Handel Meireles
Gonçalves, Cláudio Humberto
Lima, Flávio Leão
Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
title Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
title_full Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
title_fullStr Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
title_full_unstemmed Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
title_short Aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
title_sort aceruloplasminemia: a rare disease - diagnosis and treatment of two cases
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3415789/
https://www.ncbi.nlm.nih.gov/pubmed/23049345
http://dx.doi.org/10.5581/1516-8484.20110104
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