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Metabolomics of Dietary Fatty Acid Restriction in Patients with Phenylketonuria

BACKGROUND: Patients with phenylketonuria (PKU) have to follow a lifelong phenylalanine restricted diet. This type of diet markedly reduces the intake of saturated and unsaturated fatty acids especially long chain polyunsaturated fatty acids (LC-PUFA). Long-chain saturated fatty acids are substrates...

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Detalles Bibliográficos
Autores principales:	Mütze, Ulrike, Beblo, Skadi, Kortz, Linda, Matthies, Claudia, Koletzko, Berthold, Bruegel, Mathias, Rohde, Carmen, Thiery, Joachim, Kiess, Wieland, Ceglarek, Uta
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2012
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3418234/ https://www.ncbi.nlm.nih.gov/pubmed/22912778 http://dx.doi.org/10.1371/journal.pone.0043021

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