Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy o...

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Detalles Bibliográficos
Autores principales: Pavlidakey, Peter G., Mohanty, Alok, Kohler, Lisa J., Meyerson, Howard J.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2011
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3420507/
https://www.ncbi.nlm.nih.gov/pubmed/22937316
http://dx.doi.org/10.1155/2011/941637
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author Pavlidakey, Peter G.
Mohanty, Alok
Kohler, Lisa J.
Meyerson, Howard J.
author_facet Pavlidakey, Peter G.
Mohanty, Alok
Kohler, Lisa J.
Meyerson, Howard J.
author_sort Pavlidakey, Peter G.
collection PubMed
description Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma.
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spelling pubmed-34205072012-08-30 Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia Pavlidakey, Peter G. Mohanty, Alok Kohler, Lisa J. Meyerson, Howard J. Case Rep Hematol Case Report Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma. Hindawi Publishing Corporation 2011 2011-10-20 /pmc/articles/PMC3420507/ /pubmed/22937316 http://dx.doi.org/10.1155/2011/941637 Text en Copyright © 2011 Peter G. Pavlidakey et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Pavlidakey, Peter G.
Mohanty, Alok
Kohler, Lisa J.
Meyerson, Howard J.
Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
title Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
title_full Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
title_fullStr Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
title_full_unstemmed Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
title_short Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
title_sort erdheim-chester disease associated with marginal zone lymphoma and monoclonal proteinemia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3420507/
https://www.ncbi.nlm.nih.gov/pubmed/22937316
http://dx.doi.org/10.1155/2011/941637
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AT kohlerlisaj erdheimchesterdiseaseassociatedwithmarginalzonelymphomaandmonoclonalproteinemia
AT meyersonhowardj erdheimchesterdiseaseassociatedwithmarginalzonelymphomaandmonoclonalproteinemia

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