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Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour

INTRODUCTION: Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easil...

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Autores principales: Wronski, Marek, Ziarkiewicz-Wroblewska, Bogna, Slodkowski, Maciej, Cebulski, Wlodzimierz, Gornicka, Barbara, Krasnodebski, Ireneusz W.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Versita, Warsaw 2010
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3423715/
https://www.ncbi.nlm.nih.gov/pubmed/22933936
http://dx.doi.org/10.2478/v10019-010-0051-7
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author Wronski, Marek
Ziarkiewicz-Wroblewska, Bogna
Slodkowski, Maciej
Cebulski, Wlodzimierz
Gornicka, Barbara
Krasnodebski, Ireneusz W.
author_facet Wronski, Marek
Ziarkiewicz-Wroblewska, Bogna
Slodkowski, Maciej
Cebulski, Wlodzimierz
Gornicka, Barbara
Krasnodebski, Ireneusz W.
author_sort Wronski, Marek
collection PubMed
description INTRODUCTION: Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin. CASE REPORT: We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour. CONCLUSIONS: The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery.
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spelling pubmed-34237152012-08-29 Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour Wronski, Marek Ziarkiewicz-Wroblewska, Bogna Slodkowski, Maciej Cebulski, Wlodzimierz Gornicka, Barbara Krasnodebski, Ireneusz W. Radiol Oncol Case Report INTRODUCTION: Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin. CASE REPORT: We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour. CONCLUSIONS: The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery. Versita, Warsaw 2010-11-25 /pmc/articles/PMC3423715/ /pubmed/22933936 http://dx.doi.org/10.2478/v10019-010-0051-7 Text en Copyright © by Association of Radiology & Oncology http://creativecommons.org/licenses/by/3.0 This article is an open-access article distributed under the terms and conditions of the Creative Commons Attribution license (http://creativecommons.org/licenses/by/3.0/).
spellingShingle Case Report
Wronski, Marek
Ziarkiewicz-Wroblewska, Bogna
Slodkowski, Maciej
Cebulski, Wlodzimierz
Gornicka, Barbara
Krasnodebski, Ireneusz W.
Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
title Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
title_full Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
title_fullStr Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
title_full_unstemmed Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
title_short Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
title_sort mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3423715/
https://www.ncbi.nlm.nih.gov/pubmed/22933936
http://dx.doi.org/10.2478/v10019-010-0051-7
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