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Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour
INTRODUCTION: Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easil...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Versita, Warsaw
2010
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3423715/ https://www.ncbi.nlm.nih.gov/pubmed/22933936 http://dx.doi.org/10.2478/v10019-010-0051-7 |
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author | Wronski, Marek Ziarkiewicz-Wroblewska, Bogna Slodkowski, Maciej Cebulski, Wlodzimierz Gornicka, Barbara Krasnodebski, Ireneusz W. |
author_facet | Wronski, Marek Ziarkiewicz-Wroblewska, Bogna Slodkowski, Maciej Cebulski, Wlodzimierz Gornicka, Barbara Krasnodebski, Ireneusz W. |
author_sort | Wronski, Marek |
collection | PubMed |
description | INTRODUCTION: Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin. CASE REPORT: We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour. CONCLUSIONS: The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery. |
format | Online Article Text |
id | pubmed-3423715 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2010 |
publisher | Versita, Warsaw |
record_format | MEDLINE/PubMed |
spelling | pubmed-34237152012-08-29 Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour Wronski, Marek Ziarkiewicz-Wroblewska, Bogna Slodkowski, Maciej Cebulski, Wlodzimierz Gornicka, Barbara Krasnodebski, Ireneusz W. Radiol Oncol Case Report INTRODUCTION: Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare proliferative disease affecting the mesentery. It is a locally aggressive tumour that lacks metastatic potential, but the local recurrence is common. Mesenteric fibromatosis with the intestinal involvement can be easily confused with other primary gastrointestinal tumours, especially with that of the mesenchymal origin. CASE REPORT: We report a case of a 44-year-old female who presented with an abdominal mass that radiologically and pathologically mimicked a gastrointestinal stromal tumour. CONCLUSIONS: The diagnosis of mesenteric fibromatosis should always be considered in the case of mesenchymal tumours apparently originating from the bowel wall that diffusely infiltrate the mesentery. Versita, Warsaw 2010-11-25 /pmc/articles/PMC3423715/ /pubmed/22933936 http://dx.doi.org/10.2478/v10019-010-0051-7 Text en Copyright © by Association of Radiology & Oncology http://creativecommons.org/licenses/by/3.0 This article is an open-access article distributed under the terms and conditions of the Creative Commons Attribution license (http://creativecommons.org/licenses/by/3.0/). |
spellingShingle | Case Report Wronski, Marek Ziarkiewicz-Wroblewska, Bogna Slodkowski, Maciej Cebulski, Wlodzimierz Gornicka, Barbara Krasnodebski, Ireneusz W. Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
title | Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
title_full | Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
title_fullStr | Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
title_full_unstemmed | Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
title_short | Mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
title_sort | mesenteric fibromatosis with intestinal involvement mimicking a gastrointestinal stromal tumour |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3423715/ https://www.ncbi.nlm.nih.gov/pubmed/22933936 http://dx.doi.org/10.2478/v10019-010-0051-7 |
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