Malignant Perivascular Epithelioid Cell Tumor of the Esophagus

Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was prese...

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Autores principales: Fassan, Matteo, Cassaro, Mauro, Vecchiato, Massimo, Clemente, Roberto, Pennelli, Gianmaria, Merigliano, Stefano, Altavilla, Giuseppe
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2012
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3432343/
https://www.ncbi.nlm.nih.gov/pubmed/22957287
http://dx.doi.org/10.1155/2012/438505
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author Fassan, Matteo
Cassaro, Mauro
Vecchiato, Massimo
Clemente, Roberto
Pennelli, Gianmaria
Merigliano, Stefano
Altavilla, Giuseppe
author_facet Fassan, Matteo
Cassaro, Mauro
Vecchiato, Massimo
Clemente, Roberto
Pennelli, Gianmaria
Merigliano, Stefano
Altavilla, Giuseppe
author_sort Fassan, Matteo
collection PubMed
description Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are exceptional findings, clinicians should not exclude this class of tumors in the diagnostic investigation of a bulky lesion of the esophageal wall.
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spelling pubmed-34323432012-09-06 Malignant Perivascular Epithelioid Cell Tumor of the Esophagus Fassan, Matteo Cassaro, Mauro Vecchiato, Massimo Clemente, Roberto Pennelli, Gianmaria Merigliano, Stefano Altavilla, Giuseppe Case Rep Pathol Case Report Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are exceptional findings, clinicians should not exclude this class of tumors in the diagnostic investigation of a bulky lesion of the esophageal wall. Hindawi Publishing Corporation 2012 2012-08-22 /pmc/articles/PMC3432343/ /pubmed/22957287 http://dx.doi.org/10.1155/2012/438505 Text en Copyright © 2012 Matteo Fassan et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Fassan, Matteo
Cassaro, Mauro
Vecchiato, Massimo
Clemente, Roberto
Pennelli, Gianmaria
Merigliano, Stefano
Altavilla, Giuseppe
Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_full Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_fullStr Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_full_unstemmed Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_short Malignant Perivascular Epithelioid Cell Tumor of the Esophagus
title_sort malignant perivascular epithelioid cell tumor of the esophagus
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3432343/
https://www.ncbi.nlm.nih.gov/pubmed/22957287
http://dx.doi.org/10.1155/2012/438505
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