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Atypical Fibroxanthoma: An Unusual Skin Neoplasm in Xeroderma Pigmentosum

Xeroderma pigmentosum (XP) is a rare autosomal recessive disorder related to defective deoxyribonucleic acid (DNA) repair. Various cutaneous manifestations related to ultraviolet (UV) damage characterize the clinical course. Primary malignant cutaneous neoplasms like squamous cell carcinoma, basal c...

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Detalles Bibliográficos
Autores principales: Bandyopadhyay, Ranjana, Nag, Dipanwita, Bandyopadhyay, Sanjay, Sinha, Swapan Kumar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3482803/
https://www.ncbi.nlm.nih.gov/pubmed/23112360
http://dx.doi.org/10.4103/0019-5154.100493
Descripción
Sumario:Xeroderma pigmentosum (XP) is a rare autosomal recessive disorder related to defective deoxyribonucleic acid (DNA) repair. Various cutaneous manifestations related to ultraviolet (UV) damage characterize the clinical course. Primary malignant cutaneous neoplasms like squamous cell carcinoma, basal cell carcinoma and malignant melanoma have been reported. Atypical fibroxanthoma is a rare dermal neoplasm occurring in UV-damaged skin. We report an unusual case of atypical fibroxanthoma in a 20-year-old male with XP.