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Hyper IgM syndrome presenting as chronic suppurative lung disease

The Hyper-immunoglobulin M syndromes (HIGM) are a heterogeneous group of genetic disorders resulting in defects of immunoglobulin class switch recombination. Affected patients show humoral immunodeficiency and high susceptibility to opportunistic infections. Elevated serum IgM levels are the hallmar...

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Detalles Bibliográficos
Autores principales:	Montella, Silvia, Maglione, Marco, Giardino, Giuliana, Di Giorgio, Angela, Palamaro, Loredana, Mirra, Virginia, Ursini, Matilde Valeria, Salerno, Mariacarolina, Pignata, Claudio, Caffarelli, Carlo, Santamaria, Francesca
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2012
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3484017/ https://www.ncbi.nlm.nih.gov/pubmed/22992442 http://dx.doi.org/10.1186/1824-7288-38-45

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