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Fibrodysplasia ossificans progressiva: mechanisms and models of skeletal metamorphosis

Fibrodysplasia ossificans progressiva (FOP; MIM #135100) is a debilitating genetic disorder of connective tissue metamorphosis. It is characterized by malformation of the great (big) toes during embryonic skeletal development and by progressive heterotopic endochondral ossification (HEO) postnatally...

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Detalles Bibliográficos
Autores principales:	Kaplan, Frederick S., Chakkalakal, Salin A., Shore, Eileen M.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Company of Biologists Limited 2012
Materias:	Commentary
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3484858/ https://www.ncbi.nlm.nih.gov/pubmed/23115204 http://dx.doi.org/10.1242/dmm.010280

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