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A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including a...
Autores principales: | , , , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Korean Society of Cardiology
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3493809/ https://www.ncbi.nlm.nih.gov/pubmed/23170100 http://dx.doi.org/10.4070/kcj.2012.42.10.705 |
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author | Yim, Sun Mie Jang, Sung-Won Chun, Hyun Ji Kim, Su Jung Choi, Kyu Young Kwon, Beom-June Kim, Dong-Bin Cho, Eun Joo Lee, Man-Young Rho, Tai-Ho Kim, Jae-Hyung |
author_facet | Yim, Sun Mie Jang, Sung-Won Chun, Hyun Ji Kim, Su Jung Choi, Kyu Young Kwon, Beom-June Kim, Dong-Bin Cho, Eun Joo Lee, Man-Young Rho, Tai-Ho Kim, Jae-Hyung |
author_sort | Yim, Sun Mie |
collection | PubMed |
description | Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including atrial fibrillation, ventricular arrhythmias, atrioventricular block and Wolff-Parkinson-White syndrome. Herein, we describe a patient who presented with heart failure and wide-complex tachycardia. Echocardiography showed LVHT accompanied with severe mitral regurgitation. The electrophysiologic study revealed a fasciculo-ventricular accessory pathway and atrial flutter (AFL). The AFL was successfully treated with catheter ablation. |
format | Online Article Text |
id | pubmed-3493809 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2012 |
publisher | The Korean Society of Cardiology |
record_format | MEDLINE/PubMed |
spelling | pubmed-34938092012-11-20 A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter Yim, Sun Mie Jang, Sung-Won Chun, Hyun Ji Kim, Su Jung Choi, Kyu Young Kwon, Beom-June Kim, Dong-Bin Cho, Eun Joo Lee, Man-Young Rho, Tai-Ho Kim, Jae-Hyung Korean Circ J Case Report Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including atrial fibrillation, ventricular arrhythmias, atrioventricular block and Wolff-Parkinson-White syndrome. Herein, we describe a patient who presented with heart failure and wide-complex tachycardia. Echocardiography showed LVHT accompanied with severe mitral regurgitation. The electrophysiologic study revealed a fasciculo-ventricular accessory pathway and atrial flutter (AFL). The AFL was successfully treated with catheter ablation. The Korean Society of Cardiology 2012-10 2012-10-31 /pmc/articles/PMC3493809/ /pubmed/23170100 http://dx.doi.org/10.4070/kcj.2012.42.10.705 Text en Copyright © 2012 The Korean Society of Cardiology http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Yim, Sun Mie Jang, Sung-Won Chun, Hyun Ji Kim, Su Jung Choi, Kyu Young Kwon, Beom-June Kim, Dong-Bin Cho, Eun Joo Lee, Man-Young Rho, Tai-Ho Kim, Jae-Hyung A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter |
title | A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter |
title_full | A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter |
title_fullStr | A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter |
title_full_unstemmed | A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter |
title_short | A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter |
title_sort | case of left ventricular noncompaction accompanying fasciculo-ventricular accessory pathway and atrial flutter |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3493809/ https://www.ncbi.nlm.nih.gov/pubmed/23170100 http://dx.doi.org/10.4070/kcj.2012.42.10.705 |
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