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A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter

Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including a...

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Autores principales: Yim, Sun Mie, Jang, Sung-Won, Chun, Hyun Ji, Kim, Su Jung, Choi, Kyu Young, Kwon, Beom-June, Kim, Dong-Bin, Cho, Eun Joo, Lee, Man-Young, Rho, Tai-Ho, Kim, Jae-Hyung
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society of Cardiology 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3493809/
https://www.ncbi.nlm.nih.gov/pubmed/23170100
http://dx.doi.org/10.4070/kcj.2012.42.10.705
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author Yim, Sun Mie
Jang, Sung-Won
Chun, Hyun Ji
Kim, Su Jung
Choi, Kyu Young
Kwon, Beom-June
Kim, Dong-Bin
Cho, Eun Joo
Lee, Man-Young
Rho, Tai-Ho
Kim, Jae-Hyung
author_facet Yim, Sun Mie
Jang, Sung-Won
Chun, Hyun Ji
Kim, Su Jung
Choi, Kyu Young
Kwon, Beom-June
Kim, Dong-Bin
Cho, Eun Joo
Lee, Man-Young
Rho, Tai-Ho
Kim, Jae-Hyung
author_sort Yim, Sun Mie
collection PubMed
description Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including atrial fibrillation, ventricular arrhythmias, atrioventricular block and Wolff-Parkinson-White syndrome. Herein, we describe a patient who presented with heart failure and wide-complex tachycardia. Echocardiography showed LVHT accompanied with severe mitral regurgitation. The electrophysiologic study revealed a fasciculo-ventricular accessory pathway and atrial flutter (AFL). The AFL was successfully treated with catheter ablation.
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spelling pubmed-34938092012-11-20 A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter Yim, Sun Mie Jang, Sung-Won Chun, Hyun Ji Kim, Su Jung Choi, Kyu Young Kwon, Beom-June Kim, Dong-Bin Cho, Eun Joo Lee, Man-Young Rho, Tai-Ho Kim, Jae-Hyung Korean Circ J Case Report Left ventricular hypertrabeculation/noncompaction (LVHT) is an uncommon type of genetic cardiomyopathy characterized by trabeculations and recesses within the ventricular myocardium. LVHT is associated with diastolic or systolic dysfunction, thromboembolic complications, and arrhythmias, including atrial fibrillation, ventricular arrhythmias, atrioventricular block and Wolff-Parkinson-White syndrome. Herein, we describe a patient who presented with heart failure and wide-complex tachycardia. Echocardiography showed LVHT accompanied with severe mitral regurgitation. The electrophysiologic study revealed a fasciculo-ventricular accessory pathway and atrial flutter (AFL). The AFL was successfully treated with catheter ablation. The Korean Society of Cardiology 2012-10 2012-10-31 /pmc/articles/PMC3493809/ /pubmed/23170100 http://dx.doi.org/10.4070/kcj.2012.42.10.705 Text en Copyright © 2012 The Korean Society of Cardiology http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Yim, Sun Mie
Jang, Sung-Won
Chun, Hyun Ji
Kim, Su Jung
Choi, Kyu Young
Kwon, Beom-June
Kim, Dong-Bin
Cho, Eun Joo
Lee, Man-Young
Rho, Tai-Ho
Kim, Jae-Hyung
A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
title A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
title_full A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
title_fullStr A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
title_full_unstemmed A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
title_short A Case of Left Ventricular Noncompaction Accompanying Fasciculo-Ventricular Accessory Pathway and Atrial Flutter
title_sort case of left ventricular noncompaction accompanying fasciculo-ventricular accessory pathway and atrial flutter
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3493809/
https://www.ncbi.nlm.nih.gov/pubmed/23170100
http://dx.doi.org/10.4070/kcj.2012.42.10.705
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