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Mitochondrial DNA Mutations Provoke Dominant Inhibition of Mitochondrial Inner Membrane Fusion

Mitochondria are highly dynamic organelles that continuously move, fuse and divide. Mitochondrial dynamics modulate overall mitochondrial morphology and are essential for the proper function, maintenance and transmission of mitochondria and mitochondrial DNA (mtDNA). We have investigated mitochondri...

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Detalles Bibliográficos
Autores principales:	Sauvanet, Cécile, Duvezin-Caubet, Stéphane, Salin, Bénédicte, David, Claudine, Massoni-Laporte, Aurélie, di Rago, Jean-Paul, Rojo, Manuel
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2012
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3500310/ https://www.ncbi.nlm.nih.gov/pubmed/23166736 http://dx.doi.org/10.1371/journal.pone.0049639

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