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The Mitochondrial Complex I Activity Is Reduced in Cells with Impaired Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Function
Cystic fibrosis (CF) is a frequent and lethal autosomal recessive disease. It results from different possible mutations in the CFTR gene, which encodes the CFTR chloride channel. We have previously studied the differential expression of genes in CF and CF corrected cell lines, and found a reduced ex...
Autores principales: | Valdivieso, Angel G., Clauzure, Mariángeles, Marín, María C., Taminelli, Guillermo L., Massip Copiz, María M., Sánchez, Francisco, Schulman, Gustavo, Teiber, María L., Santa-Coloma, Tomás A. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3504030/ https://www.ncbi.nlm.nih.gov/pubmed/23185247 http://dx.doi.org/10.1371/journal.pone.0048059 |
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