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A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis

A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right...

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Detalles Bibliográficos
Autores principales: Mohyuddin, Ghulam Rehman, Sultan, Fatima, Khaleeq, Ghulam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3512255/
https://www.ncbi.nlm.nih.gov/pubmed/23227406
http://dx.doi.org/10.1155/2012/371490
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author Mohyuddin, Ghulam Rehman
Sultan, Fatima
Khaleeq, Ghulam
author_facet Mohyuddin, Ghulam Rehman
Sultan, Fatima
Khaleeq, Ghulam
author_sort Mohyuddin, Ghulam Rehman
collection PubMed
description A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease.
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spelling pubmed-35122552012-12-07 A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis Mohyuddin, Ghulam Rehman Sultan, Fatima Khaleeq, Ghulam Case Rep Pulmonol Case Report A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease. Hindawi Publishing Corporation 2012 2012-11-25 /pmc/articles/PMC3512255/ /pubmed/23227406 http://dx.doi.org/10.1155/2012/371490 Text en Copyright © 2012 Ghulam Rehman Mohyuddin et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Mohyuddin, Ghulam Rehman
Sultan, Fatima
Khaleeq, Ghulam
A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_full A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_fullStr A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_full_unstemmed A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_short A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
title_sort rare presentation of a rare disease: pulmonary lymphomatoid granulomatosis
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3512255/
https://www.ncbi.nlm.nih.gov/pubmed/23227406
http://dx.doi.org/10.1155/2012/371490
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