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Parry Romberg syndrome: A case report and discussion
Parry Romberg syndrome is a rare disorder of unknown etiology, seen most commonly as an asymmetry of the face, rarely affecting the limbs. Trophic malfunction of sympathetic system has been proposed as a cause. The syndrome presents with characteristic skeletal, dental, and soft tissue changes in th...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3519218/ https://www.ncbi.nlm.nih.gov/pubmed/23248475 http://dx.doi.org/10.4103/0973-029X.102498 |
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author | Madasamy, Ramasamy Jayanandan, Muruganandhan Adhavan, Uma Revathy Gopalakrishnan, Sivakumar Mahendra, Lodd |
author_facet | Madasamy, Ramasamy Jayanandan, Muruganandhan Adhavan, Uma Revathy Gopalakrishnan, Sivakumar Mahendra, Lodd |
author_sort | Madasamy, Ramasamy |
collection | PubMed |
description | Parry Romberg syndrome is a rare disorder of unknown etiology, seen most commonly as an asymmetry of the face, rarely affecting the limbs. Trophic malfunction of sympathetic system has been proposed as a cause. The syndrome presents with characteristic skeletal, dental, and soft tissue changes in the affected half of the face, with or without neurological signs and symptoms. Imaging studies sometimes reveal lesions in the brain corresponding with the neurological defects. The disfiguring nature of the disease Results in psychological disturbance and communication disorders like speech defects, as also dental anomalies. The present article reports such a case of an 8-year-old girl who presented with mainly hard tissue changes, without neurological or intraoral soft tissue changes. There has to be prompt multi-disciplinary management of such cases keeping in mind development, aesthetics, speech, and masticatory function, along with symptomatic treatment of neurological deficits. |
format | Online Article Text |
id | pubmed-3519218 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2012 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-35192182012-12-17 Parry Romberg syndrome: A case report and discussion Madasamy, Ramasamy Jayanandan, Muruganandhan Adhavan, Uma Revathy Gopalakrishnan, Sivakumar Mahendra, Lodd J Oral Maxillofac Pathol Case Report Parry Romberg syndrome is a rare disorder of unknown etiology, seen most commonly as an asymmetry of the face, rarely affecting the limbs. Trophic malfunction of sympathetic system has been proposed as a cause. The syndrome presents with characteristic skeletal, dental, and soft tissue changes in the affected half of the face, with or without neurological signs and symptoms. Imaging studies sometimes reveal lesions in the brain corresponding with the neurological defects. The disfiguring nature of the disease Results in psychological disturbance and communication disorders like speech defects, as also dental anomalies. The present article reports such a case of an 8-year-old girl who presented with mainly hard tissue changes, without neurological or intraoral soft tissue changes. There has to be prompt multi-disciplinary management of such cases keeping in mind development, aesthetics, speech, and masticatory function, along with symptomatic treatment of neurological deficits. Medknow Publications & Media Pvt Ltd 2012 /pmc/articles/PMC3519218/ /pubmed/23248475 http://dx.doi.org/10.4103/0973-029X.102498 Text en Copyright: © Journal of Oral and Maxillofacial Pathology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Madasamy, Ramasamy Jayanandan, Muruganandhan Adhavan, Uma Revathy Gopalakrishnan, Sivakumar Mahendra, Lodd Parry Romberg syndrome: A case report and discussion |
title | Parry Romberg syndrome: A case report and discussion |
title_full | Parry Romberg syndrome: A case report and discussion |
title_fullStr | Parry Romberg syndrome: A case report and discussion |
title_full_unstemmed | Parry Romberg syndrome: A case report and discussion |
title_short | Parry Romberg syndrome: A case report and discussion |
title_sort | parry romberg syndrome: a case report and discussion |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3519218/ https://www.ncbi.nlm.nih.gov/pubmed/23248475 http://dx.doi.org/10.4103/0973-029X.102498 |
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