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Fenofibrate Therapy in Carnitine Palmitoyl Transferase Type 2 Deficiency
Bezafibrate therapy has been shown to improve beta-oxidation of fatty acids and to reduce episodes of rhabdomyolysis in patients with carnitine palmitoyltransferase type-2 (CPT2) deficiency. We report the efficacy of fenofibrate in a patient with CPT2 deficiency, in whom beta-oxidation was improved...
Autores principales: | Hamilton-Craig, I., Yudi, M., Johnson, L., Jayasinghe, R. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi Publishing Corporation
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3521633/ https://www.ncbi.nlm.nih.gov/pubmed/23326270 http://dx.doi.org/10.1155/2012/163173 |
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