Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature

Angioedema related to a deficiency in the C1-inhibitor protein is characterized by its lack of response to therapies including antihistamine, steroids, and epinephrine. In the case of laryngeal edema, mortality rate is approximately 30 percent. The first case of the acquired form of angioedema relat...

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Detalles Bibliográficos
Autores principales: Hallak, Bassel, Konu, Propser, Lang, Florian, Simon, Christian, Monnier, Philippe
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2012
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3523597/
https://www.ncbi.nlm.nih.gov/pubmed/23304594
http://dx.doi.org/10.1155/2012/405824
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author Hallak, Bassel
Konu, Propser
Lang, Florian
Simon, Christian
Monnier, Philippe
author_facet Hallak, Bassel
Konu, Propser
Lang, Florian
Simon, Christian
Monnier, Philippe
author_sort Hallak, Bassel
collection PubMed
description Angioedema related to a deficiency in the C1-inhibitor protein is characterized by its lack of response to therapies including antihistamine, steroids, and epinephrine. In the case of laryngeal edema, mortality rate is approximately 30 percent. The first case of the acquired form of angioedema related to a deficiency in C1-inhibitor was published in 1972. In our paper, we present a case of an acquired form of angioedema of the oropharyngeal region secondary to the simultaneous occurrence of two causative factors: neutralization of C1-inhibitor by an autoantibody and the use of an angiotensin convertin enzyme inhibitor.
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spelling pubmed-35235972013-01-09 Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature Hallak, Bassel Konu, Propser Lang, Florian Simon, Christian Monnier, Philippe Case Rep Otolaryngol Case Report Angioedema related to a deficiency in the C1-inhibitor protein is characterized by its lack of response to therapies including antihistamine, steroids, and epinephrine. In the case of laryngeal edema, mortality rate is approximately 30 percent. The first case of the acquired form of angioedema related to a deficiency in C1-inhibitor was published in 1972. In our paper, we present a case of an acquired form of angioedema of the oropharyngeal region secondary to the simultaneous occurrence of two causative factors: neutralization of C1-inhibitor by an autoantibody and the use of an angiotensin convertin enzyme inhibitor. Hindawi Publishing Corporation 2012 2012-12-10 /pmc/articles/PMC3523597/ /pubmed/23304594 http://dx.doi.org/10.1155/2012/405824 Text en Copyright © 2012 Bassel Hallak et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Hallak, Bassel
Konu, Propser
Lang, Florian
Simon, Christian
Monnier, Philippe
Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature
title Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature
title_full Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature
title_fullStr Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature
title_full_unstemmed Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature
title_short Acquired Form of Angioedema of the Head and Neck Related to a Deficiency in C1-Inhibitor: A Case Report with a Review of the Literature
title_sort acquired form of angioedema of the head and neck related to a deficiency in c1-inhibitor: a case report with a review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3523597/
https://www.ncbi.nlm.nih.gov/pubmed/23304594
http://dx.doi.org/10.1155/2012/405824
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