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FSHD Myotubes with Different Phenotypes Exhibit Distinct Proteomes
Facioscapulohumeral muscular dystrophy (FSHD) is a progressive muscle disorder linked to a contraction of the D4Z4 repeat array in the 4q35 subtelomeric region. This deletion induces epigenetic modifications that affect the expression of several genes located in the vicinity. In each D4Z4 element, w...
Autores principales: | Tassin, Alexandra, Leroy, Baptiste, Laoudj-Chenivesse, Dalila, Wauters, Armelle, Vanderplanck, Céline, Le Bihan, Marie-Catherine, Coppée, Frédérique, Wattiez, Ruddy, Belayew, Alexandra |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3525578/ https://www.ncbi.nlm.nih.gov/pubmed/23272181 http://dx.doi.org/10.1371/journal.pone.0051865 |
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