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Two-year follow-up of Sanfilippo Disease patients treated with a genistein-rich isoflavone extract: Assessment of effects on cognitive functions and general status of patients

BACKGROUND: Mucopolysaccharidoses (MPS) are inherited metabolic disorders caused by deficiencies in enzymes involved in degradation of glycosaminoglycans. MPS type III (Sanfilippo disease) is clinically characterized mainly by progressive and severe behavioral disturbances and cognitive dysfunction....

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Detalles Bibliográficos
Autores principales:	Piotrowska, Ewa, Jakobkiewicz-Banecka, Joanna, Maryniak, Agnieszka, Tylki-Szymanska, Anna, Puk, Ewa, Liberek, Anna, Wegrzyn, Alicja, Czartoryska, Barbara, Slominska-Wojewodzka, Monika, Węgrzyn, Grzegorz
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	International Scientific Literature, Inc. 2011
Materias:	Clinical Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3539518/ https://www.ncbi.nlm.nih.gov/pubmed/21455105 http://dx.doi.org/10.12659/MSM.881715

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