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Olmsted Syndrome
Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyper...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi Publishing Corporation
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3540698/ https://www.ncbi.nlm.nih.gov/pubmed/23320205 http://dx.doi.org/10.1155/2012/927305 |
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author | Elise Tonoli, Renata De Villa, Damiê Hübner Frainer, Renata Pizzarro Meneghello, Luana Ricachnevsky, Nelson de Quadros, Maurício |
author_facet | Elise Tonoli, Renata De Villa, Damiê Hübner Frainer, Renata Pizzarro Meneghello, Luana Ricachnevsky, Nelson de Quadros, Maurício |
author_sort | Elise Tonoli, Renata |
collection | PubMed |
description | Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment. |
format | Online Article Text |
id | pubmed-3540698 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2012 |
publisher | Hindawi Publishing Corporation |
record_format | MEDLINE/PubMed |
spelling | pubmed-35406982013-01-14 Olmsted Syndrome Elise Tonoli, Renata De Villa, Damiê Hübner Frainer, Renata Pizzarro Meneghello, Luana Ricachnevsky, Nelson de Quadros, Maurício Case Rep Dermatol Med Case Report Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment. Hindawi Publishing Corporation 2012 2012-12-23 /pmc/articles/PMC3540698/ /pubmed/23320205 http://dx.doi.org/10.1155/2012/927305 Text en Copyright © 2012 Renata Elise Tonoli et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Elise Tonoli, Renata De Villa, Damiê Hübner Frainer, Renata Pizzarro Meneghello, Luana Ricachnevsky, Nelson de Quadros, Maurício Olmsted Syndrome |
title | Olmsted Syndrome |
title_full | Olmsted Syndrome |
title_fullStr | Olmsted Syndrome |
title_full_unstemmed | Olmsted Syndrome |
title_short | Olmsted Syndrome |
title_sort | olmsted syndrome |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3540698/ https://www.ncbi.nlm.nih.gov/pubmed/23320205 http://dx.doi.org/10.1155/2012/927305 |
work_keys_str_mv | AT elisetonolirenata olmstedsyndrome AT devilladamie olmstedsyndrome AT hubnerfrainerrenata olmstedsyndrome AT pizzarromeneghelloluana olmstedsyndrome AT ricachnevskynelson olmstedsyndrome AT dequadrosmauricio olmstedsyndrome |