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Decremental Responses to Repetitive Nerve Stimulation in X-Linked Bulbospinal Muscular Atrophy

BACKGROUND AND PURPOSE: X-linked bulbospinal muscular atrophy (X-BSMA) is characterized by bulbar and spinal muscular weakness and fasciculations. Although X-BSMA is a motor neuronopathy, there are several reports of myasthenic symptoms or decremental responses to repetitive nerve stimulation (RNS)....

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Detalles Bibliográficos
Autores principales:	Kim, Jee Young, Park, Kee Duk, Kim, Seung-Min, Sunwoo, Il Nam
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Korean Neurological Association 2013
Materias:	Original Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3543907/ https://www.ncbi.nlm.nih.gov/pubmed/23346158 http://dx.doi.org/10.3988/jcn.2013.9.1.32

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