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Sod1 Deficiency Reduces Incubation Time in Mouse Models of Prion Disease
Prion infections, causing neurodegenerative conditions such as Creutzfeldt-Jakob disease and kuru in humans, scrapie in sheep and BSE in cattle are characterised by prolonged and variable incubation periods that are faithfully reproduced in mouse models. Incubation time is partly determined by genet...
Autores principales: | Akhtar, Shaheen, Grizenkova, Julia, Wenborn, Adam, Hummerich, Holger, Fernandez de Marco, Mar, Brandner, Sebastian, Collinge, John, Lloyd, Sarah E. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3551847/ https://www.ncbi.nlm.nih.gov/pubmed/23349894 http://dx.doi.org/10.1371/journal.pone.0054454 |
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