Different molecular mechanisms involved in spontaneous and oxidative stress-induced mitochondrial fragmentation in tripeptidyl peptidase-1 (TPP-1)-deficient fibroblasts

NCLs (neuronal ceroid lipofuscinoses) form a group of eight inherited autosomal recessive diseases characterized by the intralysosomal accumulation of autofluorescent pigments, called ceroids. Recent data suggest that the pathogenesis of NCL is associated with the appearance of fragmented mitochondr...

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Detalles Bibliográficos
Autores principales: Van Beersel, Guillaume, Tihon, Eliane, Demine, Stéphane, Hamer, Isabelle, Jadot, Michel, Arnould, Thierry
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Portland Press Ltd. 2013
Materias:
Original Paper
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3566540/
https://www.ncbi.nlm.nih.gov/pubmed/23249249
http://dx.doi.org/10.1042/BSR20120104

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3566540/
https://www.ncbi.nlm.nih.gov/pubmed/23249249
http://dx.doi.org/10.1042/BSR20120104

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