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Congenital nasal pyriform aperture stenosis: diagnosis and management
BACKGROUND: Congenital nasal pyriform aperture stenosis is a rare and potentially lethal form of airway obstruction in newborns. Immediate recognition and appropriate therapy are mandatory for this potentially life-threating condition. This anomaly may present as an isolated malformation or may be a...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3574011/ https://www.ncbi.nlm.nih.gov/pubmed/22731387 http://dx.doi.org/10.1186/1824-7288-38-28 |
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author | Sesenna, Enrico Leporati, Massimiliano Brevi, Bruno Oretti, Gabriele Ferri, Andrea |
author_facet | Sesenna, Enrico Leporati, Massimiliano Brevi, Bruno Oretti, Gabriele Ferri, Andrea |
author_sort | Sesenna, Enrico |
collection | PubMed |
description | BACKGROUND: Congenital nasal pyriform aperture stenosis is a rare and potentially lethal form of airway obstruction in newborns. Immediate recognition and appropriate therapy are mandatory for this potentially life-threating condition. This anomaly may present as an isolated malformation or may be associated with other cranial-facial anomalies. Clinically, CNPS shows unspecific symptoms of nasal airway obstruction such as apnoic crisis, episodic cyanosis and inability to nurse. The purpose of this report is to present author's experience in the surgical management of this rare pathology in 3 patients. PATIENTS AND METHODS: Three cases of congenital nasal pyriform aperture stenosis were reviewed for presentation of the disorder, management and effectiveness of the surgical treatment. RESULTS: All the patients underwent a surgical correction of the pyriform aperture stenosis using a sublabial approach followed by nasal stenting. During the follow-up no cases of restenosis, respiratory failure or cyanosis were detected. CONCLUSIONS: Congenital pyriform aperture stenosis should be suspected in newborns with clinical signs of severe nasal obstruction associated with a difficulty to pass a small catheter though the anterior nasal valve. Timely recognition is mandatory to prevent a potential deadly outcome. Surgical correction of the stenosis though a sublabial approach followed by a nasal stenting revealed to be most effective treatment for these patients. |
format | Online Article Text |
id | pubmed-3574011 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2012 |
publisher | BioMed Central |
record_format | MEDLINE/PubMed |
spelling | pubmed-35740112013-02-16 Congenital nasal pyriform aperture stenosis: diagnosis and management Sesenna, Enrico Leporati, Massimiliano Brevi, Bruno Oretti, Gabriele Ferri, Andrea Ital J Pediatr Case Report BACKGROUND: Congenital nasal pyriform aperture stenosis is a rare and potentially lethal form of airway obstruction in newborns. Immediate recognition and appropriate therapy are mandatory for this potentially life-threating condition. This anomaly may present as an isolated malformation or may be associated with other cranial-facial anomalies. Clinically, CNPS shows unspecific symptoms of nasal airway obstruction such as apnoic crisis, episodic cyanosis and inability to nurse. The purpose of this report is to present author's experience in the surgical management of this rare pathology in 3 patients. PATIENTS AND METHODS: Three cases of congenital nasal pyriform aperture stenosis were reviewed for presentation of the disorder, management and effectiveness of the surgical treatment. RESULTS: All the patients underwent a surgical correction of the pyriform aperture stenosis using a sublabial approach followed by nasal stenting. During the follow-up no cases of restenosis, respiratory failure or cyanosis were detected. CONCLUSIONS: Congenital pyriform aperture stenosis should be suspected in newborns with clinical signs of severe nasal obstruction associated with a difficulty to pass a small catheter though the anterior nasal valve. Timely recognition is mandatory to prevent a potential deadly outcome. Surgical correction of the stenosis though a sublabial approach followed by a nasal stenting revealed to be most effective treatment for these patients. BioMed Central 2012-06-26 /pmc/articles/PMC3574011/ /pubmed/22731387 http://dx.doi.org/10.1186/1824-7288-38-28 Text en Copyright ©2012 Sesenna et al.; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License ( http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Sesenna, Enrico Leporati, Massimiliano Brevi, Bruno Oretti, Gabriele Ferri, Andrea Congenital nasal pyriform aperture stenosis: diagnosis and management |
title | Congenital nasal pyriform aperture stenosis: diagnosis and management |
title_full | Congenital nasal pyriform aperture stenosis: diagnosis and management |
title_fullStr | Congenital nasal pyriform aperture stenosis: diagnosis and management |
title_full_unstemmed | Congenital nasal pyriform aperture stenosis: diagnosis and management |
title_short | Congenital nasal pyriform aperture stenosis: diagnosis and management |
title_sort | congenital nasal pyriform aperture stenosis: diagnosis and management |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3574011/ https://www.ncbi.nlm.nih.gov/pubmed/22731387 http://dx.doi.org/10.1186/1824-7288-38-28 |
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