Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome

Marfan syndrome is an inherited, connective-tissue disorder transmitted as an autosomal dominant trait. Cardinal features of the disorder include tall stature, ectopia lentis, mitral valve prolapse, aortic root dilatation, and aortic dissection. Pectus excavatum may exist as an isolated lesion or in...

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Autores principales: Kansara, Bhuvnesh, Singh, Ajmer, Girotra, Samir, Iyer, K S
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3590552/
https://www.ncbi.nlm.nih.gov/pubmed/23493844
http://dx.doi.org/10.4103/0970-9185.105812
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author Kansara, Bhuvnesh
Singh, Ajmer
Girotra, Samir
Iyer, K S
author_facet Kansara, Bhuvnesh
Singh, Ajmer
Girotra, Samir
Iyer, K S
author_sort Kansara, Bhuvnesh
collection PubMed
description Marfan syndrome is an inherited, connective-tissue disorder transmitted as an autosomal dominant trait. Cardinal features of the disorder include tall stature, ectopia lentis, mitral valve prolapse, aortic root dilatation, and aortic dissection. Pectus excavatum may exist as an isolated lesion or in association with a genetic syndrome such as Marfan syndrome. We report the successful management of a simultaneous correction of pectus excavatum and the underlying cardiovascular diseases.
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spelling pubmed-35905522013-03-14 Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome Kansara, Bhuvnesh Singh, Ajmer Girotra, Samir Iyer, K S J Anaesthesiol Clin Pharmacol Case Report Marfan syndrome is an inherited, connective-tissue disorder transmitted as an autosomal dominant trait. Cardinal features of the disorder include tall stature, ectopia lentis, mitral valve prolapse, aortic root dilatation, and aortic dissection. Pectus excavatum may exist as an isolated lesion or in association with a genetic syndrome such as Marfan syndrome. We report the successful management of a simultaneous correction of pectus excavatum and the underlying cardiovascular diseases. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3590552/ /pubmed/23493844 http://dx.doi.org/10.4103/0970-9185.105812 Text en Copyright: © Journal of Anaesthesiology Clinical Pharmacology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Kansara, Bhuvnesh
Singh, Ajmer
Girotra, Samir
Iyer, K S
Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome
title Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome
title_full Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome
title_fullStr Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome
title_full_unstemmed Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome
title_short Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome
title_sort combined bentall and modified ravitch procedures in a patient with marfan syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3590552/
https://www.ncbi.nlm.nih.gov/pubmed/23493844
http://dx.doi.org/10.4103/0970-9185.105812
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