Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney

Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond we...

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Detalles Bibliográficos
Autores principales: Kim, Sunchan, Kim, Tae Gu, Choi, Seung-Kwon, Kim, Myung Joon, Min, Gyeong Eun, Lee, Hyung-Lae, Yoo, Koo Han
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Urological Association 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3604578/
https://www.ncbi.nlm.nih.gov/pubmed/23525099
http://dx.doi.org/10.4111/kju.2013.54.3.209
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author Kim, Sunchan
Kim, Tae Gu
Choi, Seung-Kwon
Kim, Myung Joon
Min, Gyeong Eun
Lee, Hyung-Lae
Yoo, Koo Han
author_facet Kim, Sunchan
Kim, Tae Gu
Choi, Seung-Kwon
Kim, Myung Joon
Min, Gyeong Eun
Lee, Hyung-Lae
Yoo, Koo Han
author_sort Kim, Sunchan
collection PubMed
description Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.
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spelling pubmed-36045782013-03-22 Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney Kim, Sunchan Kim, Tae Gu Choi, Seung-Kwon Kim, Myung Joon Min, Gyeong Eun Lee, Hyung-Lae Yoo, Koo Han Korean J Urol Case Report Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids. The Korean Urological Association 2013-03 2013-03-15 /pmc/articles/PMC3604578/ /pubmed/23525099 http://dx.doi.org/10.4111/kju.2013.54.3.209 Text en © The Korean Urological Association, 2013 http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Kim, Sunchan
Kim, Tae Gu
Choi, Seung-Kwon
Kim, Myung Joon
Min, Gyeong Eun
Lee, Hyung-Lae
Yoo, Koo Han
Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
title Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
title_full Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
title_fullStr Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
title_full_unstemmed Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
title_short Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
title_sort immunoglobulin g4-related systemic sclerosing disease: a case involving the ureter and kidney
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3604578/
https://www.ncbi.nlm.nih.gov/pubmed/23525099
http://dx.doi.org/10.4111/kju.2013.54.3.209
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