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Leaky ryanodine receptors in β-sarcoglycan deficient mice: a potential common defect in muscular dystrophy

BACKGROUND: Disruption of the sarcolemma-associated dystrophin-glycoprotein complex underlies multiple forms of muscular dystrophy, including Duchenne muscular dystrophy and sarcoglycanopathies. A hallmark of these disorders is muscle weakness. In a murine model of Duchenne muscular dystrophy, mdx m...

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Detalles Bibliográficos
Autores principales:	Andersson, Daniel C, Meli, Albano C, Reiken, Steven, Betzenhauser, Matthew J, Umanskaya, Alisa, Shiomi, Takayuki, D’Armiento, Jeanine, Marks, Andrew R
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2012
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3605002/ https://www.ncbi.nlm.nih.gov/pubmed/22640601 http://dx.doi.org/10.1186/2044-5040-2-9

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