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Bronchoscopic observation of unusual deformities of bronchial cartilage and subsequent airway narrowing in respiratory relapsing polychondritis

BACKGROUND: Relapsing polychondritis (RP) is a rare inflammatory disease characterized by recurrent chondritis and inflammation of other proteoglycan-rich tissues. An RP patient with co-existing respiratory tract problems could have a poor prognosis. CASE REPORT: We reported a case of RP died with r...

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Detalles Bibliográficos
Autores principales: Kawano, Tetsuya, Matsuse, Hiroto, Kinoshita, Naoe, Tsuchida, Tomoko, Nishino, Tomoya, Fukushima, Chizu, Hayashi, Tomayoshi, Kohno, Shigeru
Formato: Online Artículo Texto
Lenguaje:English
Publicado: International Scientific Literature, Inc. 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3616182/
https://www.ncbi.nlm.nih.gov/pubmed/23569504
http://dx.doi.org/10.12659/AJCR.883091
Descripción
Sumario:BACKGROUND: Relapsing polychondritis (RP) is a rare inflammatory disease characterized by recurrent chondritis and inflammation of other proteoglycan-rich tissues. An RP patient with co-existing respiratory tract problems could have a poor prognosis. CASE REPORT: We reported a case of RP died with recurrent suffocation. At the early stage in this case, unusual deformities of bronchial cartilage were observed. Following systemic corticosteroid therapy, these deformities disappeared, and typical diffuse mucosal edema and dynamic collapse of airways developed. CONCLUSIONS: These bronchoscopic abnormalities could be the early stage of RP.