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Functional and histopathological identification of the respiratory failure in a DMSXL transgenic mouse model of myotonic dystrophy

Acute and chronic respiratory failure is one of the major and potentially life-threatening features in individuals with myotonic dystrophy type 1 (DM1). Despite several clinical demonstrations showing respiratory problems in DM1 patients, the mechanisms are still not completely understood. This stud...

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Detalles Bibliográficos
Autores principales:	Panaite, Petrica-Adrian, Kuntzer, Thierry, Gourdon, Geneviève, Lobrinus, Johannes Alexander, Barakat-Walter, Ibtissam
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Company of Biologists Limited 2013
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3634646/ https://www.ncbi.nlm.nih.gov/pubmed/23180777 http://dx.doi.org/10.1242/dmm.010512

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