Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome

Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-...

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Detalles Bibliográficos
Autores principales: Bonilla-Abadía, Fabio, Pérez, Manuel A., Muñoz-Buitrón, Evelyn, Rosales, Joaquín D., Cañas, Carlos A., Tobón, Gabriel J.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3655507/
https://www.ncbi.nlm.nih.gov/pubmed/23710406
http://dx.doi.org/10.1155/2013/831708
Descripción
Sumario:Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-fold compared to healthy population, mainly of the MALT lymphoma type. This case reports a 52-year-old woman with pSS developing a progressively growing mass at face and neck compatible with blastoid variant mantle cell lymphoma and a fatal outcome.

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