Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome

Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-...

Descripción completa

Detalles Bibliográficos
Autores principales: Bonilla-Abadía, Fabio, Pérez, Manuel A., Muñoz-Buitrón, Evelyn, Rosales, Joaquín D., Cañas, Carlos A., Tobón, Gabriel J.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3655507/
https://www.ncbi.nlm.nih.gov/pubmed/23710406
http://dx.doi.org/10.1155/2013/831708
_version_ 1782269888142770176
author Bonilla-Abadía, Fabio
Pérez, Manuel A.
Muñoz-Buitrón, Evelyn
Rosales, Joaquín D.
Cañas, Carlos A.
Tobón, Gabriel J.
author_facet Bonilla-Abadía, Fabio
Pérez, Manuel A.
Muñoz-Buitrón, Evelyn
Rosales, Joaquín D.
Cañas, Carlos A.
Tobón, Gabriel J.
author_sort Bonilla-Abadía, Fabio
collection PubMed
description Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-fold compared to healthy population, mainly of the MALT lymphoma type. This case reports a 52-year-old woman with pSS developing a progressively growing mass at face and neck compatible with blastoid variant mantle cell lymphoma and a fatal outcome.
format Online
Article
Text
id pubmed-3655507
institution National Center for Biotechnology Information
language English
publishDate 2013
publisher Hindawi Publishing Corporation
record_format MEDLINE/PubMed
spelling pubmed-36555072013-05-24 Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome Bonilla-Abadía, Fabio Pérez, Manuel A. Muñoz-Buitrón, Evelyn Rosales, Joaquín D. Cañas, Carlos A. Tobón, Gabriel J. Case Rep Rheumatol Case Report Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-fold compared to healthy population, mainly of the MALT lymphoma type. This case reports a 52-year-old woman with pSS developing a progressively growing mass at face and neck compatible with blastoid variant mantle cell lymphoma and a fatal outcome. Hindawi Publishing Corporation 2013 2013-04-23 /pmc/articles/PMC3655507/ /pubmed/23710406 http://dx.doi.org/10.1155/2013/831708 Text en Copyright © 2013 Fabio Bonilla-Abadía et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Bonilla-Abadía, Fabio
Pérez, Manuel A.
Muñoz-Buitrón, Evelyn
Rosales, Joaquín D.
Cañas, Carlos A.
Tobón, Gabriel J.
Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
title Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
title_full Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
title_fullStr Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
title_full_unstemmed Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
title_short Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome
title_sort fatal blastoid variant mantle cell lymphoma in a patient with sjögren's syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3655507/
https://www.ncbi.nlm.nih.gov/pubmed/23710406
http://dx.doi.org/10.1155/2013/831708
work_keys_str_mv AT bonillaabadiafabio fatalblastoidvariantmantlecelllymphomainapatientwithsjogrenssyndrome
AT perezmanuela fatalblastoidvariantmantlecelllymphomainapatientwithsjogrenssyndrome
AT munozbuitronevelyn fatalblastoidvariantmantlecelllymphomainapatientwithsjogrenssyndrome
AT rosalesjoaquind fatalblastoidvariantmantlecelllymphomainapatientwithsjogrenssyndrome
AT canascarlosa fatalblastoidvariantmantlecelllymphomainapatientwithsjogrenssyndrome
AT tobongabrielj fatalblastoidvariantmantlecelllymphomainapatientwithsjogrenssyndrome

Ejemplares similares