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Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?

Fixed dystonia is a disabling disorder mainly affecting young women who develop fixed abnormal limb postures and pain after apparently minor peripheral injury. There is continued debate regarding its pathophysiology and management. We report 5 cases of fixed dystonia in patients who sought amputatio...

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Autores principales: Edwards, Mark J, Alonso-Canovas, Araceli, Schrag, Arnette, Bloem, Bastiaan R, Thompson, Philip D, Bhatia, Kailash
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wiley Subscription Services, Inc., A Wiley Company 2011
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3664409/
https://www.ncbi.nlm.nih.gov/pubmed/21484872
http://dx.doi.org/10.1002/mds.23671
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author Edwards, Mark J
Alonso-Canovas, Araceli
Schrag, Arnette
Bloem, Bastiaan R
Thompson, Philip D
Bhatia, Kailash
author_facet Edwards, Mark J
Alonso-Canovas, Araceli
Schrag, Arnette
Bloem, Bastiaan R
Thompson, Philip D
Bhatia, Kailash
author_sort Edwards, Mark J
collection PubMed
description Fixed dystonia is a disabling disorder mainly affecting young women who develop fixed abnormal limb postures and pain after apparently minor peripheral injury. There is continued debate regarding its pathophysiology and management. We report 5 cases of fixed dystonia in patients who sought amputation of the affected limb. We place these cases in the context of previous reports of patients with healthy limbs and patients with chronic regional pain syndrome who have sought amputation. Our cases, combined with recent data regarding disorders of mental rotation in patients with fixed dystonia, as well as previous data regarding body integrity identity disorder and amputations sought by patients with chronic regional pain syndrome, raise the possibility that patients with fixed dystonia might have a deficit in body schema that predisposes them to developing fixed dystonia and drives some to seek amputation. The outcome of amputation in fixed dystonia is invariably unfavorable. © 2011 Movement Disorder Society
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spelling pubmed-36644092013-06-03 Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder? Edwards, Mark J Alonso-Canovas, Araceli Schrag, Arnette Bloem, Bastiaan R Thompson, Philip D Bhatia, Kailash Mov Disord Research Articles Fixed dystonia is a disabling disorder mainly affecting young women who develop fixed abnormal limb postures and pain after apparently minor peripheral injury. There is continued debate regarding its pathophysiology and management. We report 5 cases of fixed dystonia in patients who sought amputation of the affected limb. We place these cases in the context of previous reports of patients with healthy limbs and patients with chronic regional pain syndrome who have sought amputation. Our cases, combined with recent data regarding disorders of mental rotation in patients with fixed dystonia, as well as previous data regarding body integrity identity disorder and amputations sought by patients with chronic regional pain syndrome, raise the possibility that patients with fixed dystonia might have a deficit in body schema that predisposes them to developing fixed dystonia and drives some to seek amputation. The outcome of amputation in fixed dystonia is invariably unfavorable. © 2011 Movement Disorder Society Wiley Subscription Services, Inc., A Wiley Company 2011-07 2011-04-11 /pmc/articles/PMC3664409/ /pubmed/21484872 http://dx.doi.org/10.1002/mds.23671 Text en Copyright © 2011 Movement Disorder Society http://creativecommons.org/licenses/by/2.5/ Re-use of this article is permitted in accordance with the Creative Commons Deed, Attribution 2.5, which does not permit commercial exploitation.
spellingShingle Research Articles
Edwards, Mark J
Alonso-Canovas, Araceli
Schrag, Arnette
Bloem, Bastiaan R
Thompson, Philip D
Bhatia, Kailash
Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?
title Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?
title_full Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?
title_fullStr Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?
title_full_unstemmed Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?
title_short Limb Amputations in Fixed Dystonia: A Form of Body Integrity Identity Disorder?
title_sort limb amputations in fixed dystonia: a form of body integrity identity disorder?
topic Research Articles
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3664409/
https://www.ncbi.nlm.nih.gov/pubmed/21484872
http://dx.doi.org/10.1002/mds.23671
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