A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava

Ewing's sarcomas and peripheral primitive neuroectodermal tumors (ES/PNETs) are high grade malignant neoplasms. These malignancies are characterized by a chromosome 22 rearrangement, arise from bone or soft tissue, predominantly affect children and young adults, and are grouped in the Ewing fam...

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Autores principales: Reali, Alessia, Mortellaro, Gianluca, Allis, Simona, Trevisiol, Edoardo, Anglesio, Silvia Maria, Bartoncini, Sara, Redda, Maria Grazia Ruo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3667441/
https://www.ncbi.nlm.nih.gov/pubmed/23741276
http://dx.doi.org/10.4103/1817-1737.109834
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author Reali, Alessia
Mortellaro, Gianluca
Allis, Simona
Trevisiol, Edoardo
Anglesio, Silvia Maria
Bartoncini, Sara
Redda, Maria Grazia Ruo
author_facet Reali, Alessia
Mortellaro, Gianluca
Allis, Simona
Trevisiol, Edoardo
Anglesio, Silvia Maria
Bartoncini, Sara
Redda, Maria Grazia Ruo
author_sort Reali, Alessia
collection PubMed
description Ewing's sarcomas and peripheral primitive neuroectodermal tumors (ES/PNETs) are high grade malignant neoplasms. These malignancies are characterized by a chromosome 22 rearrangement, arise from bone or soft tissue, predominantly affect children and young adults, and are grouped in the Ewing family of tumors. Multimodality treatment programs are the treatment of choice. Primary localization of ES/PNET in the mediastinum is extremely rare. We describe a case of ES/PNET presenting as a mediastinal mass with tracheal compression and initial signs of superior vena cava in a 66-year-old woman.
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spelling pubmed-36674412013-06-05 A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava Reali, Alessia Mortellaro, Gianluca Allis, Simona Trevisiol, Edoardo Anglesio, Silvia Maria Bartoncini, Sara Redda, Maria Grazia Ruo Ann Thorac Med Case Report Ewing's sarcomas and peripheral primitive neuroectodermal tumors (ES/PNETs) are high grade malignant neoplasms. These malignancies are characterized by a chromosome 22 rearrangement, arise from bone or soft tissue, predominantly affect children and young adults, and are grouped in the Ewing family of tumors. Multimodality treatment programs are the treatment of choice. Primary localization of ES/PNET in the mediastinum is extremely rare. We describe a case of ES/PNET presenting as a mediastinal mass with tracheal compression and initial signs of superior vena cava in a 66-year-old woman. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3667441/ /pubmed/23741276 http://dx.doi.org/10.4103/1817-1737.109834 Text en Copyright: © Annals of Thoracic Medicine http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Reali, Alessia
Mortellaro, Gianluca
Allis, Simona
Trevisiol, Edoardo
Anglesio, Silvia Maria
Bartoncini, Sara
Redda, Maria Grazia Ruo
A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
title A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
title_full A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
title_fullStr A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
title_full_unstemmed A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
title_short A case of primary mediastinal Ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
title_sort case of primary mediastinal ewing's sarcoma / primitive neuroectodermal tumor presenting with initial compression of superior vena cava
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3667441/
https://www.ncbi.nlm.nih.gov/pubmed/23741276
http://dx.doi.org/10.4103/1817-1737.109834
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