Cargando…

Alport's Syndrome in Pregnancy

Background. Alport's syndrome is an X-linked hereditary disorder affecting the glomerular basement membrane associated with ocular and hearing defects. In women, the disease is much less severe compared to that in men. However, women with Alport's syndrome can have an accelerated form of t...

Descripción completa

Detalles Bibliográficos
Autores principales: Mehta, Suchita, Saifan, Chadi, Abdellah, Marie, Choueiry, Rita, Nasr, Rabih, El-Sayegh, Suzanne
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3686057/
https://www.ncbi.nlm.nih.gov/pubmed/23861686
http://dx.doi.org/10.1155/2013/374020
_version_ 1782273748867481600
author Mehta, Suchita
Saifan, Chadi
Abdellah, Marie
Choueiry, Rita
Nasr, Rabih
El-Sayegh, Suzanne
author_facet Mehta, Suchita
Saifan, Chadi
Abdellah, Marie
Choueiry, Rita
Nasr, Rabih
El-Sayegh, Suzanne
author_sort Mehta, Suchita
collection PubMed
description Background. Alport's syndrome is an X-linked hereditary disorder affecting the glomerular basement membrane associated with ocular and hearing defects. In women, the disease is much less severe compared to that in men. However, women with Alport's syndrome can have an accelerated form of their disease during pregnancy with worsening of kidney function and can also develop preeclampsia. There are only four described cases of Alport's syndrome in pregnancy. Case Presentation. 20-year-old woman with a history of Alport's syndrome, which during pregnancy worsened resulting in hypertension, proteinuria, and acute kidney injury. Fortunately, there was complete resolution of the proteinuria and kidney injury with delivery, and the patient did not require any renal replacement therapy. Conclusion. One of the four reported cases had an accelerated form of the disease during pregnancy with rapid progression of kidney injury and end-stage renal disease. There are no definite guidelines to monitor these patients during pregnancy. Further studies are required to understand the exact pathophysiology of kidney damage that occurs in pregnant women with Alport's syndrome. This may give us some insight into the prognostic predictors, so that we can monitor these women more thoroughly and prevent adverse outcomes.
format Online
Article
Text
id pubmed-3686057
institution National Center for Biotechnology Information
language English
publishDate 2013
publisher Hindawi Publishing Corporation
record_format MEDLINE/PubMed
spelling pubmed-36860572013-07-16 Alport's Syndrome in Pregnancy Mehta, Suchita Saifan, Chadi Abdellah, Marie Choueiry, Rita Nasr, Rabih El-Sayegh, Suzanne Case Rep Med Case Report Background. Alport's syndrome is an X-linked hereditary disorder affecting the glomerular basement membrane associated with ocular and hearing defects. In women, the disease is much less severe compared to that in men. However, women with Alport's syndrome can have an accelerated form of their disease during pregnancy with worsening of kidney function and can also develop preeclampsia. There are only four described cases of Alport's syndrome in pregnancy. Case Presentation. 20-year-old woman with a history of Alport's syndrome, which during pregnancy worsened resulting in hypertension, proteinuria, and acute kidney injury. Fortunately, there was complete resolution of the proteinuria and kidney injury with delivery, and the patient did not require any renal replacement therapy. Conclusion. One of the four reported cases had an accelerated form of the disease during pregnancy with rapid progression of kidney injury and end-stage renal disease. There are no definite guidelines to monitor these patients during pregnancy. Further studies are required to understand the exact pathophysiology of kidney damage that occurs in pregnant women with Alport's syndrome. This may give us some insight into the prognostic predictors, so that we can monitor these women more thoroughly and prevent adverse outcomes. Hindawi Publishing Corporation 2013 2013-06-03 /pmc/articles/PMC3686057/ /pubmed/23861686 http://dx.doi.org/10.1155/2013/374020 Text en Copyright © 2013 Suchita Mehta et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Mehta, Suchita
Saifan, Chadi
Abdellah, Marie
Choueiry, Rita
Nasr, Rabih
El-Sayegh, Suzanne
Alport's Syndrome in Pregnancy
title Alport's Syndrome in Pregnancy
title_full Alport's Syndrome in Pregnancy
title_fullStr Alport's Syndrome in Pregnancy
title_full_unstemmed Alport's Syndrome in Pregnancy
title_short Alport's Syndrome in Pregnancy
title_sort alport's syndrome in pregnancy
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3686057/
https://www.ncbi.nlm.nih.gov/pubmed/23861686
http://dx.doi.org/10.1155/2013/374020
work_keys_str_mv AT mehtasuchita alportssyndromeinpregnancy
AT saifanchadi alportssyndromeinpregnancy
AT abdellahmarie alportssyndromeinpregnancy
AT choueiryrita alportssyndromeinpregnancy
AT nasrrabih alportssyndromeinpregnancy
AT elsayeghsuzanne alportssyndromeinpregnancy